Publications

For links to PubMed Citations, please view our complete list of publications here.

 

PMIDAuthorsJournal (Link to PubMed abstract)Title
29437698Hull, Rebecca L; Gibson, Ronald L; McNamara, Sharon; Deutsch, Gail H; Fligner, Corinne L; Frevert, Charles W; Ramsey, Bonnie W; Sanda, SrinathDiabetes Care; 2018 Feb 01Islet Interleukin-1β Immunoreactivity Is an Early Feature of Cystic Fibrosis That May Contribute to β-Cell Failure.
29378945Matamouros S, Hayden HS, Hager KR, Brittnacher MJ, Lachance K, Weiss EJ, Pope CE, Imhaus AF, McNally CP, Borenstein E, Hoffman LR, Miller SIProc Natl Acad Sci U S A; 2018 Jan 29Adaptation of commensal proliferating Escherichia coli to the intestinal tract of young children with cystic fibrosis.
29192813Sack, Cora S; Goss, Christopher HAnn Am Thorac Soc; 2017 DecYet Again, Air Pollution Impacts Lung Health.
29177135Maillé, Émilie; Ruffin, Manon; Adam, Damien; Messaoud, Hatem; Lafayette, Shantelle L; McKay, Geoffrey; Nguyen, Dao; Brochiero, EmmanuelleFront Cell Infect Microbiol; 2017Quorum Sensing Down-Regulation Counteracts the Negative Impact of Pseudomonas aeruginosa on CFTR Channel Expression, Function and Rescue in Human Airway Epithelial Cells.
29176494Gelfond, Daniel; Heltshe, Sonya L; Skalland, Michelle; Heubi, James E; Kloster, Margaret; Leung, Daniel H; Ramsey, Bonnie W; Borowitz, Drucy; BONUS Study InvestigatorsJ Pediatr Gastroenterol Nutr; 2017 Nov 15Pancreatic Enzyme Replacement Therapy use in infants with Cystic Fibrosis Diagnosed by Newborn Screening.
29170074Heltshe, Sonya L; West, Natalie E; VanDevanter, Donald R; Sanders, D B; Beckett, Valeria V; Flume, Patrick A; Goss, Christopher H; STOP Study GroupContemp Clin Trials; 2018 JanStudy design considerations for the Standardized Treatment of Pulmonary Exacerbations 2 (STOP2): A trial to compare intravenous antibiotic treatment durations in CF.
29144467Whiteley M, Diggle SP, Greenberg EPNature; 2017 Nov 15Progress in and promise of bacterial quorum sensing research.
29110966Heltshe, S L; Khan, U; Beckett, V; Baines, A; Emerson, J; Sanders, D B; Gibson, R L; Morgan, W; Rosenfeld, MJ Cyst Fibros; 2017 Oct 27Longitudinal development of initial, chronic and mucoid Pseudomonas aeruginosa infection in young children with cystic fibrosis.
29078392White, Paul; Joshi, Amar; Rassam, Patrice; Housden, Nicholas G; Kaminska, Renata; Goult, Jonathan D; Redfield, Christina; McCaughey, Laura C; Walker, Daniel; Mohammed, Shabaz; Kleanthous, ColinProc Natl Acad Sci U S A; 2017 Nov 07Exploitation of an iron transporter for bacterial protein antibiotic import.
29065453Passos da Silva, Daniel; Schofield, Melissa C; Parsek, Matthew R; Tseng, Boo ShanPathogens; 2017 Oct 21An Update on the Sociomicrobiology of Quorum Sensing in Gram-Negative Biofilm Development.
28982193Shrestha, Chandra L; Assani, Kaivon D; Rinehardt, Hannah; Albastroiu, Florentina; Zhang, Shuzhong; Shell, Richard; Amer, Amal O; Schlesinger, Larry S; Kopp, Benjamin TPLoS One; 2017Cysteamine-mediated clearance of antibiotic-resistant pathogens in human cystic fibrosis macrophages.
28879065Long ME, Gong K, Eddy WE, Liles WC, and Manicone AMPneumonia (Nathan); 2017 Sep 5Pharmacologic Inhibition of MEK1/2 Reduces Lung Inflammation without Impairing Bacterial Clearance in Experimental Pseudomonas aeruginosa Pneumonia.
28808129Toussaint, Jean-Paul; Farrell-Sherman, Anna; Feldman, Tamar Perla; Smalley, Nicole E; Schaefer, Amy L; Greenberg, E Peter; Dandekar, Ajai AJ Bacteriol; 2017 Nov 01Gene Duplication in Pseudomonas aeruginosa Improves Growth on Adenosine.
28743819Scholz, Rebecca L; Greenberg, E PeterMBio; 2017 Jul 25Positive Autoregulation of an Acyl-Homoserine Lactone Quorum-Sensing Circuit Synchronizes the Population Response.
28622619Gao, Chunying; Bergagnini-Kolev, Mackenzie C; Liao, Michael Z; Wang, Zhican; Wong, Timothy; Calamia, Justina C; Lin, Yvonne S; Mao, Qingcheng; Thummel, Kenneth EJ Chromatogr B Analyt Technol Biomed Life Sci; 2017 Jun 09Simultaneous quantification of 25-hydroxyvitamin D3-3-sulfate and 25-hydroxyvitamin D3-3-glucuronide in human serum and plasma using liquid chromatography-tandem mass spectrometry coupled with DAPTAD-derivatization.
28608719Lechtzin, Noah; Mayer-Hamblett, Nicole; West, Natalie E; Allgood, Sarah; Wilhelm, Ellen; Khan, Umer; Aitken, Moira L; Ramsey, Bonnie W; Boyle, Michael P; Mogayzel Jr, Peter J; Gibson, Ronald L; Orenstein, David; Milla, Carlos; Clancy, John P; Antony, VeenAm J Respir Crit Care Med; 2017 11 01Home Monitoring of Patients with Cystic Fibrosis to Identify and Treat Acute Pulmonary Exacerbations. eICE Study Results.
28570601Ketelboeter, Laura M; Bardy, Sonia LPLoS One; 2017Characterization of 2-(2-nitro-4-trifluoromethylbenzoyl)-1,3-cyclohexanedione resistance in pyomelanogenic Pseudomonas aeruginosa DKN343.
28500076Eddy, William E; Gong, Ke-Qin; Bell, Bryan; Parks, William C; Ziegler, Steven F; Manicone, Anne MJ Immunol; 2017 Jun 15Stat5 Is Required for CD103(+) Dendritic Cell and Alveolar Macrophage Development and Protection from Lung Injury.
28460885Sanders, Don B; Solomon, George M; Beckett, Valeria V; West, Natalie E; Daines, Cori L; Heltshe, Sonya L; VanDevanter, Donald R; Spahr, Jonathan E; Gibson, Ronald L; Nick, Jerry A; Marshall, Bruce C; Flume, Patrick A; Goss, Christopher H; STOP Study GroupJ Cyst Fibros; 2017 SepStandardized Treatment of Pulmonary Exacerbations (STOP) study: Observations at the initiation of intravenous antibiotics for cystic fibrosis pulmonary exacerbations.
28459323Ramsey, Bonnie W; Welsh, Michael JAm J Respir Crit Care Med; 2017 05 01AJRCCM: 100-Year Anniversary. Progress along the Pathway of Discovery Leading to Treatment and Cure of Cystic Fibrosis.
28446704Karig, David K; Bessling, Seneca; Thielen, Peter; Zhang, Sherry; Wolfe, JoshuaJ R Soc Interface; 2017 AprPreservation of protein expression systems at elevated temperatures for portable therapeutic production.
28437538Leung, Daniel H; Heltshe, Sonya L; Borowitz, Drucy; Gelfond, Daniel; Kloster, Margaret; Heubi, James E; Stalvey, Michael; Ramsey, Bonnie W; Baby Observational and Nutrition Study (BONUS) Investigators of the Cystic Fibrosis Foundation Therapeutics DevelopJAMA Pediatr; 2017 Jun 01Effects of Diagnosis by Newborn Screening for Cystic Fibrosis on Weight and Length in the First Year of Life.
28329304Somayaji, Ranjani; Goss, Christopher H; Khan, Umer; Neradilek, Moni; Neuzil, Kathleen M; Ortiz, Justin RClin Infect Dis; 2017 Jun 15Cystic fibrosis pulmonary exacerbations attributable to respiratory syncytial virus and influenza: a population-based study.
28300821Gelfond, Daniel; Heltshe, Sonya; Ma, Changxing; Rowe, Steven M; Frederick, Carla; Uluer, Ahmet; Sicilian, Leonard; Konstan, Michael; Tullis, Elizabeth; Roach, R N Christine; Griffin, Katherine; Joseloff, Elizabeth; Borowitz, DrucyClin Transl Gastroenterol; 2017 Mar 16Impact of CFTR Modulation on Intestinal pH, Motility, and Clinical Outcomes in Patients With Cystic Fibrosis and the G551D Mutation.
28288488Stephenson, Anne L; Sykes, Jenna; Stanojevic, Sanja; Quon, Bradley S; Marshall, Bruce C; Petren, Kristofer; Ostrenga, Josh; Fink, Aliza K; Elbert, Alexander; Goss, Christopher HAnn Intern Med; 2017 Apr 18Survival Comparison of Patients With Cystic Fibrosis in Canada and the United States: A Population-Based Cohort Study.
28222269Hisert, Katherine B; Heltshe, Sonya L; Pope, Christopher; Jorth, Peter; Wu, Xia; Edwards, Rachael M; Radey, Matthew; Accurso, Frank J; Wolter, Daniel J; Cooke, Gordon; Adam, Ryan J; Carter, Suzanne; Grogan, Brenda; Launspach, Janice L; Donnelly, Seamas C;Am J Respir Crit Care Med; 2017 Jun 15Restoring Cystic Fibrosis Transmembrane Conductance Regulator Function Reduces Airway Bacteria and Inflammation in People with Cystic Fibrosis and Chronic Lung Infections.
28215711Muhlebach, Marianne S; Clancy, J P; Heltshe, Sonya L; Ziady, Assem; Kelley, Tom; Accurso, Frank; Pilewski, Joseph; Mayer-Hamblett, Nicole; Joseloff, Elizabeth; Sagel, Scott DJ Cyst Fibros; 2016 NovBiomarkers for cystic fibrosis drug development.
28193635Whiteley, Aaron T; Ruhland, Brittany R; Edrozo, Mauna B; Reniere, Michelle LInfect Immun; 2017 MayA Redox-Responsive Transcription Factor Is Critical for Pathogenesis and Aerobic Growth of Listeria monocytogenes.
28190780Heltshe, Sonya L; Godfrey, Emily M; Josephy, Tatiana; Aitken, Moira L; Taylor-Cousar, Jennifer LJ Cyst Fibros; 2017 NovPregnancy among cystic fibrosis women in the era of CFTR modulators.
28143919Stalvey, Michael S; Pace, Jesse; Niknian, Minoo; Higgins, Mark N; Tarn, Valerie; Davis, Joy; Heltshe, Sonya L; Rowe, Steven MPediatrics; 2017 FebGrowth in Prepubertal Children With Cystic Fibrosis Treated With Ivacaftor.
28126911Cogen, Jonathan D; Oron, Assaf P; Gibson, Ronald L; Hoffman, Lucas R; Kronman, Matthew P; Ong, Thida; Rosenfeld, MargaretPediatrics; 2017 FebCharacterization of Inpatient Cystic Fibrosis Pulmonary Exacerbations.
28117136Szczesniak, Rhonda; Heltshe, Sonya L; Stanojevic, Sanja; Mayer-Hamblett, NicoleJ Cyst Fibros; 2017 MayUse of FEV1 in cystic fibrosis epidemiologic studies and clinical trials: A statistical perspective for the clinical researcher.
28115168Ramos, Kathleen J; Quon, Bradley S; Heltshe, Sonya L; Mayer-Hamblett, Nicole; Lease, Erika D; Aitken, Moira L; Weiss, Noel S; Goss, Christopher HChest; 2017 JunHeterogeneity in Survival in Adult Patients With Cystic Fibrosis With FEV1 < 30% of Predicted in the United States.
28103851Ramos, Kathleen J; Somayaji, Ranjani; Lease, Erika D; Goss, Christopher H; Aitken, Moira LBMC Pulm Med; 2017 Jan 19Cystic fibrosis physicians' perspectives on the timing of referral for lung transplant evaluation: a survey of physicians in the United States.
28093527Assani, Kaivon; Shrestha, Chandra L; Robledo-Avila, Frank; Rajaram, Murugesan V; Partida-Sanchez, Santiago; Schlesinger, Larry S; Kopp, Benjamin TJ Immunol; 2017 Mar 01Human Cystic Fibrosis Macrophages Have Defective Calcium-Dependent Protein Kinase C Activation of the NADPH Oxidase, an Effect Augmented by Burkholderia cenocepacia.
28025037Nichols, Dave P; Happoldt, Carrie L; Bratcher, Preston E; Caceres, Silvia M; Chmiel, James F; Malcolm, Kenneth C; Saavedra, Milene T; Saiman, Lisa; Taylor-Cousar, Jennifer L; Nick, Jerry AJ Cyst Fibros; 2017 MayImpact of azithromycin on the clinical and antimicrobial effectiveness of tobramycin in the treatment of cystic fibrosis.
28003382Long, Matthew E; Eddy, William E; Gong, Ke-Qin; Lovelace-Macon, Lara L; McMahan, Ryan S; Charron, Jean; Liles, W Conrad; Manicone, Anne MJ Immunol; 2017 Jan 15MEK1/2 Inhibition Promotes Macrophage Reparative Properties.
27942594Ge, Lingyin; Habiel, David M; Hansbro, Phil M; Kim, Richard Y; Gharib, Sina A; Edelman, Jeffery D; Königshoff, Melanie; Parimon, Tanyalak; Brauer, Rena; Huang, Ying; Allen, Jenieke; Jiang, Dianhua; Kurkciyan, Adrianne A; Mizuno, Takako; Stripp, Barry R; Noble, Paul W; Hogaboam, Cory M; Chen, PeterJCI Insight; 2016 Dec 08miR-323a-3p regulates lung fibrosis by targeting multiple profibrotic pathways.
27929111Martínez, Eriel; Campos-Gómez, JavierNat Commun; 2016 Dec 08Oxylipins produced by Pseudomonas aeruginosa promote biofilm formation and virulence.
27927212Crull, Mathew R; Ramos, Kathleen J; Caldwell, Ellen; Mayer-Hamblett, Nicole; Aitken, Moira L; Goss, Christopher HBMC Pulm Med; 2016 Dec 07Change in Pseudomonas aeruginosa prevalence in cystic fibrosis adults over time.
27868360Miller, Christine L; Van Laar, Tricia A; Chen, Tsute; Karna, S L Rajasekhar; Chen, Ping; You, Tao; Leung, Kai PMicrobiologyopen; 2017 JunGlobal transcriptome responses including small RNAs during mixed-species interactions with methicillin-resistant Staphylococcus aureus and Pseudomonas aeruginosa.
27855208Floyd, Madison; Winn, Matthew; Cullen, Christian; Sil, Payel; Chassaing, Benoit; Yoo, Dae-Goon; Gewirtz, Andrew T; Goldberg, Joanna B; McCarter, Linda L; Rada, BalázsPLoS Pathog; 2016 NovSwimming Motility Mediates the Formation of Neutrophil Extracellular Traps Induced by Flagellated Pseudomonas aeruginosa.
27852955Muhlebach, Marianne Sponer; Beckett, Valeria; Popowitch, Elena; Miller, Melissa B; Baines, Arthur; Mayer-Hamblett, Nicole; Zemanick, Edith T; Hoover, Wynton C; VanDalfsen, Jill M; Campbell, Preston; Goss, Christopher H; STAR-too study teamThorax; 2017 AprMicrobiological efficacy of early MRSA treatment in cystic fibrosis in a randomised controlled trial.
27846621Alkhateeb, Alaa A; Mancl, Lloyd A; Presland, Richard B; Rothen, Marilynn L; Chi, Donald LCaries Res; 2017Unstimulated Saliva-Related Caries Risk Factors in Individuals with Cystic Fibrosis: A Cross-Sectional Analysis of Unstimulated Salivary Flow, pH, and Buffering Capacity.
27805836Milla, Carlos E; Ratjen, Felix; Marigowda, Gautham; Liu, Fang; Waltz, David; Rosenfeld, Margaret; VX13-809-011 Part B Investigator Group *Am J Respir Crit Care Med; 2017 Apr 01Lumacaftor/Ivacaftor in Patients Aged 6-11 Years with Cystic Fibrosis and Homozygous for F508del-CFTR.
27795361Secor, Patrick R; Michaels, Lia A; Smigiel, Kate S; Rohani, Maryam G; Jennings, Laura K; Hisert, Katherine B; Arrigoni, Allison; Braun, Kathleen R; Birkland, Timothy P; Lai, Ying; Hallstrand, Teal S; Bollyky, Paul L; Singh, Pradeep K; Parks, William CInfect Immun; 2017 JanFilamentous Bacteriophage Produced by Pseudomonas aeruginosa Alters the Inflammatory Response and Promotes Noninvasive Infection In Vivo.
27793338Ramos, Kathleen J; Sack, Coralynn S; Mitchell, Kristina H; Goss, Christopher H; Starr, Jacqueline RJ Pediatr; 2017 JanCystic Fibrosis is Associated with Adverse Neonatal Outcomes in Washington State, 1996-2013.
27710011Heltshe, Sonya L; Cogen, Jonathan; Ramos, Kathleen J; Goss, Christopher HAm J Respir Crit Care Med; 2017 Apr 15Cystic Fibrosis: The Dawn of a New Therapeutic Era.
27706847Peek, James; Roman, Joseph; Moran, Graham R; Christendat, DineshMol Microbiol; 2017 01Structurally diverse dehydroshikimate dehydratase variants participate in microbial quinate catabolism.
27703072Feltner, John B; Wolter, Daniel J; Pope, Christopher E; Groleau, Marie-Christine; Smalley, Nicole E; Greenberg, E Peter; Mayer-Hamblett, Nicole; Burns, Jane; Déziel, Eric; Hoffman, Lucas R; Dandekar, Ajai AMBio; 2016 Oct 04LasR Variant Cystic Fibrosis Isolates Reveal an Adaptable Quorum-Sensing Hierarchy in Pseudomonas aeruginosa.
27662102Rogers, Geraint B; Narkewicz, Michael R; Hoffman, Lucas RPediatr Pulmonol; 2016 OctThe CF gastrointestinal microbiome: Structure and clinical impact.
27627472Goss, Christopher HAnn Am Thorac Soc; 2016 SepWith Every Upside, There Is a Downside: Chest Radiation and Survivors of Childhood Cancers.
27518252VanDevanter, Donald R; Heltshe, Sonya L; LiPuma, John JAnn Am Thorac Soc; 2016 NovPotential for Therapeutic Benefit among Cystic Fibrosis Populations Excluded from Clinical Trials or Labeling of Marketed Therapies.
27469186Ong, Thida; Ramsey, Bonnie WPediatr Clin North Am; 2016 08New Therapeutic Approaches to Modulate and Correct Cystic Fibrosis Transmembrane Conductance Regulator.
27469179Zemanick, Edith T; Hoffman, Lucas RPediatr Clin North Am; 2016 08Cystic Fibrosis: Microbiology and Host Response.
27430253Miller, Christine L; Romero, Manuel; Karna, S L Rajasekhar; Chen, Tsute; Heeb, Stephan; Leung, Kai PBMC Microbiol; 2016 Jul 19RsmW, Pseudomonas aeruginosa small non-coding RsmA-binding RNA upregulated in biofilm versus planktonic growth conditions.
27391011Brittnacher, Mitchell J; Heltshe, Sonya L; Hayden, Hillary S; Radey, Matthew C; Weiss, Eli J; Damman, Christopher J; Zisman, Timothy L; Suskind, David L; Miller, Samuel IPLoS One; 2016GUTSS: An Alignment-Free Sequence Comparison Method for Use in Human Intestinal Microbiome and Fecal Microbiota Transplantation Analysis.
27388563Marsh, R L; Kaestli, M; Chang, A B; Binks, M J; Pope, C E; Hoffman, L R; Smith-Vaughan, H CMicrobiome; 2016 Jul 07The microbiota in bronchoalveolar lavage from young children with chronic lung disease includes taxa present in both the oropharynx and nasopharynx.
27248587Sack, Cora S; Goss, Christopher HAm J Respir Crit Care Med; 2016 Jun 01Nature versus Nurture: Does Genetic Ancestry Alter the Effect of Air Pollution in Children with Asthma?
27231351Xu, Linghui; Venkataramani, Prabhadevi; Ding, Yichen; Liu, Yang; Deng, Yinyue; Yong, Grace Lisi; Xin, Lingyi; Ye, Ruijuan; Zhang, Lianhui; Yang, Liang; Liang, Zhao-XunJ Biol Chem; 2016 Jul 29A Cyclic di-GMP-binding Adaptor Protein Interacts with Histidine Kinase to Regulate Two-component Signaling.
27222468Armbruster, Catherine R; Wolter, Daniel J; Mishra, Meenu; Hayden, Hillary S; Radey, Matthew C; Merrihew, Gennifer; MacCoss, Michael J; Burns, Jane; Wozniak, Daniel J; Parsek, Matthew R; Hoffman, Lucas RMBio; 2016 May 24Staphylococcus aureus Protein A Mediates Interspecies Interactions at the Cell Surface of Pseudomonas aeruginosa.
27178322Ruffin, Manon; Bilodeau, Claudia; Maillé, Émilie; LaFayette, Shantelle L; McKay, Geoffrey A; Trinh, Nguyen Thu Ngan; Beaudoin, Trevor; Desrosiers, Martin-Yvon; Rousseau, Simon; Nguyen, Dao; Brochiero, EmmanuelleFASEB J; 2016 09Quorum-sensing inhibition abrogates the deleterious impact of Pseudomonas aeruginosa on airway epithelial repair.
27119970Hocquet, Didier; Petitjean, Marie; Rohmer, Laurence; Valot, Benoît; Kulasekara, Hemantha D; Bedel, Elodie; Bertrand, Xavier; Plésiat, Patrick; Köhler, Thilo; Pantel, Alix; Jacobs, Michael A; Hoffman, Lucas R; Miller, Samuel IEnviron Microbiol; 2016 OctPyomelanin-producing Pseudomonas aeruginosa selected during chronic infections have a large chromosomal deletion which confers resistance to pyocins.
27035067Hisert, Katherine B; Schoenfelt, Kelly Q; Cooke, Gordon; Grogan, Brenda; Launspach, Jan L; Gallagher, Charles G; Donnelly, Seamas C; Welsh, Michael J; Singh, Pradeep K; McKone, Edward F; Becker, LevAm J Respir Cell Mol Biol; 2016 AprIvacaftor-Induced Proteomic Changes Suggest Monocyte Defects May Contribute to the Pathogenesis of Cystic Fibrosis.
26959387Brauer R, Ge L, Schlesinger SY, Birkland TP, Huang Y, Parimon T, Lee V, McKinney BL, McGuire JK, Parks WC, Chen PAm J Respir Crit Care Med; 2016 Aug 1Syndecan-1 Attenuates Lung Injury during Influenza Infection by Potentiating c-Met Signaling to Suppress Epithelial Apoptosis.
26956590Hayden, Hillary S; Matamouros, Susana; Hager, Kyle R; Brittnacher, Mitchell J; Rohmer, Laurence; Radey, Matthew C; Weiss, Eli J; Kim, Katie B; Jacobs, Michael A; Sims-Day, Elizabeth H; Yue, Min; Zaidi, Mussaret B; Schifferli, Dieter M; Manning, Shannon D; Walson, Judd L; Miller, Samuel IMBio; 2016Genomic Analysis of Salmonella enterica Serovar Typhimurium Characterizes Strain Diversity for Recent U.S. Salmonellosis Cases and Identifies Mutations Linked to Loss of Fitness under Nitrosative and Oxidative Stress.
26940651Manor, Ohad; Levy, Roie; Pope, Christopher E; Hayden, Hillary S; Brittnacher, Mitchell J; Carr, Rogan; Radey, Matthew C; Hager, Kyle R; Heltshe, Sonya L; Ramsey, Bonnie W; Miller, Samuel I; Hoffman, Lucas R; Borenstein, ElhananSci Rep; 2016 Mar 04Metagenomic evidence for taxonomic dysbiosis and functional imbalance in the gastrointestinal tracts of children with cystic fibrosis.
26934670Gill, Sean E; Nadler, Samuel T; Li, Qinglang; Frevert, Charles W; Park, Pyong Woo; Chen, Peter; Parks, William CAm J Respir Cell Mol Biol; 2016 AugShedding of Syndecan-1/CXCL1 Complexes by Matrix Metalloproteinase 7 Functions as an Epithelial Checkpoint of Neutrophil Activation.
26903594Mayer-Hamblett, Nicole; Boyle, Michael; VanDevanter, DonaldThorax; 2016 MayAdvancing clinical development pathways for new CFTR modulators in cystic fibrosis.
26774758Goss, Christopher H; VanDevanter, Donald RJ Cyst Fibros; 2016 JanCFTR modulators and pregnancy: Our work has only just begun.
26769012Heltshe, Sonya L; Goss, Christopher HThorax; 2016 FebOptimising treatment of CF pulmonary exacerbation: a tough nut to crack.
26729501Precit, Mimi R; Wolter, Daniel J; Griffith, Adam; Emerson, Julia; Burns, Jane L; Hoffman, Lucas RAntimicrob Agents Chemother; 2016 Jan 04Optimized In Vitro Antibiotic Susceptibility Testing Method for Small-Colony Variant Staphylococcus aureus.
26704622Ramos, Kathleen J; Quon, Bradley S; Psoter, Kevin J; Lease, Erika D; Mayer-Hamblett, Nicole; Aitken, Moira L; Goss, Christopher HJ Cyst Fibros; 2016 MarPredictors of non-referral of patients with cystic fibrosis for lung transplant evaluation in the United States.
26665020Ruddy, Jennifer; Emerson, Julia; McNamara, Sharon; Genatossio, Alan; Breuner, Cora; Weber, Tracy; Rosenfeld, MargaretGlob Adv Health Med; 2015 NovYoga as a Therapy for Adolescents and Young Adults With Cystic Fibrosis: A Pilot Study.
26567508Secor, Patrick R; Sweere, Johanna M; Michaels, Lia A; Malkovskiy, Andrey V; Lazzareschi, Daniel; Katznelson, Ethan; Rajadas, Jayakumar; Birnbaum, Michael E; Arrigoni, Allison; Braun, Kathleen R; Evanko, Stephen P; Stevens, David A; Kaminsky, Werner; Singh, Pradeep K; Parks, William C; Bollyky, Paul LCell Host Microbe; 2015 Nov 11Filamentous Bacteriophage Promote Biofilm Assembly and Function.
26547590Davis, Stephanie D; Ratjen, Felix; Brumback, Lyndia C; Johnson, Robin C; Filbrun, Amy G; Kerby, Gwendolyn S; Panitch, Howard B; Donaldson, Scott H; Rosenfeld, Margaret; ISIS Study GroupJ Cyst Fibros; 2016 MayInfant lung function tests as endpoints in the ISIS multicenter clinical trial in cystic fibrosis.
26517411Sack, Coralynn; Goss, Christopher HAm J Respir Crit Care Med; 2015 Nov 01It Starts at the Beginning: Effect of Particulate Matter In Utero.
26492139Hmelo, Laura R; Borlee, Bradley R; Almblad, Henrik; Love, Michelle E; Randall, Trevor E; Tseng, Boo Shan; Lin, Chuyang; Irie, Yasuhiko; Storek, Kelly M; Yang, Jaeun Jane; Siehnel, Richard J; Howell, P Lynne; Singh, Pradeep K; Tolker-Nielsen, Tim; Parsek, Matthew R; Schweizer, Herbert P; Harrison, Joe JNat Protoc; 2015 NovPrecision-engineering the Pseudomonas aeruginosa genome with two-step allelic exchange.
26483767Freschi, Luca; Jeukens, Julie; Kukavica-Ibrulj, Irena; Boyle, Brian; Dupont, Marie-Josée; Laroche, Jérôme; Larose, Stéphane; Maaroufi, Halim; Fothergill, Joanne L; Moore, Matthew; Winsor, Geoffrey L; Aaron, Shawn D; Barbeau, Jean; Bell, Scott C; Burns, Jane L; Camara, Miguel; Cantin, André; Charette, Steve J; Dewar, Ken; Déziel, Éric; Grimwood, Keith; Hancock, Robert E W; Harrison, Joe J; Heeb, Stephan; Jelsbak, Lars; Jia, Baofeng; Kenna, Dervla T; Kidd, Timothy J; Klockgether, Jens; Lam, Joseph S; Lamont, Iain L; Lewenza, Shawn; Loman, Nick; Malouin, François; Manos, Jim; McArthur, Andrew G; McKeown, Josie; Milot, Julie; Naghra, Hardeep; Nguyen, Dao; Pereira, Sheldon K; Perron, Gabriel G; Pirnay, Jean-Paul; Rainey, Paul B; Rousseau, Simon; Santos, Pedro M; Stephenson, Anne; Taylor, Véronique; Turton, Jane F; Waglechner, Nicholas; Williams, Paul; Thrane, Sandra W; Wright, Gerard D; Brinkman, Fiona S L; Tucker, Nicholas P; Tümmler, Burkhard; Winstanley, Craig; Levesque, Roger CFront Microbiol; 2015Clinical utilization of genomics data produced by the international Pseudomonas aeruginosa consortium.
26459101Fowler, Randal C; Hanson, Nancy DMicrobiologyopen; 2015 DecThe OpdQ porin of Pseudomonas aeruginosa is regulated by environmental signals associated with cystic fibrosis including nitrate-induced regulation involving the NarXL two-component system.
26457326LaFayette, Shantelle L; Houle, Daniel; Beaudoin, Trevor; Wojewodka, Gabriella; Radzioch, Danuta; Hoffman, Lucas R; Burns, Jane L; Dandekar, Ajai A; Smalley, Nicole E; Chandler, Josephine R; Zlosnik, James E; Speert, David P; Bernier, Joanie; Matouk, Elias; Brochiero, Emmanuelle; Rousseau, Simon; Nguyen, DaoSci Adv; 2015 JulCystic fibrosis-adapted Pseudomonas aeruginosa quorum sensing lasR mutants cause hyperinflammatory responses.
26434789Sykes, Jenna; Stanojevic, Sanja; Goss, Christopher H; Quon, Bradley S; Marshall, Bruce C; Petren, Kristofer; Ostrenga, Josh; Fink, Aliza; Elbert, Alexander; Stephenson, Anne LJ Clin Epidemiol; 2016 FebA standardized approach to estimating survival statistics for population-based cystic fibrosis registry cohorts.
26385570Snyder, Jessica M; Washington, Ida M; Birkland, Timothy; Chang, Mary Y; Frevert, Charles WJ Histochem Cytochem; 2015 DecCorrelation of Versican Expression, Accumulation, and Degradation during Embryonic Development by Quantitative Immunohistochemistry.
26382879Ketelboeter, Laura M; Bardy, Sonia LJ Vis Exp; 2015Methods to Inhibit Bacterial Pyomelanin Production and Determine the Corresponding Increase in Sensitivity to Oxidative Stress.
26336603Heltshe, Sonya L; Saiman, Lisa; Popowitch, Elena B; Miller, Melissa B; Kloster, Margaret; Thompson, Valeria; Ferkol, Thomas W; Hoover, Wynton C; Schechter, Michael S; Muhlebach, Marianne SJ Pediatric Infect Dis Soc; 2015 SepOutcomes and Treatment of Chronic Methicillin-Resistant Staphylococcus aureus Differs by Staphylococcal Cassette Chromosome mec (SCCmec) Type in Children With Cystic Fibrosis.
26335957Sawicki, Gregory S; Goss, Christopher HPediatr Pulmonol; 2015 OctTackling the increasing complexity of CF care.
26311845Jennings, Laura K; Storek, Kelly M; Ledvina, Hannah E; Coulon, Charlène; Marmont, Lindsey S; Sadovskaya, Irina; Secor, Patrick R; Tseng, Boo Shan; Scian, Michele; Filloux, Alain; Wozniak, Daniel J; Howell, P Lynne; Parsek, Matthew RProc Natl Acad Sci U S A; 2015 Sep 8Pel is a cationic exopolysaccharide that cross-links extracellular DNA in the Pseudomonas aeruginosa biofilm matrix.
26311173Lundgren, Benjamin R; Harris, Joshua R; Sarwar, Zaara; Scheel, Ryan A; Nomura, Christopher TMicrobiology; 2015 NovThe metabolism of (R)-3-hydroxybutyrate is regulated by the enhancer-binding protein PA2005 and the alternative sigma factor RpoN in Pseudomonas aeruginosa PAO1.
26299432Jorth, Peter; Staudinger, Benjamin J; Wu, Xia; Hisert, Katherine B; Hayden, Hillary; Garudathri, Jayanthi; Harding, Christopher L; Radey, Matthew C; Rezayat, Amir; Bautista, Gilbert; Berrington, William R; Goddard, Amanda F; Zheng, Chunxiang; Angermeyer, Angus; Brittnacher, Mitchell J; Kitzman, Jacob; Shendure, Jay; Fligner, Corinne L; Mittler, John; Aitken, Moira L; Manoil, Colin; Bruce, James E; Yahr, Timothy L; Singh, Pradeep KCell Host Microbe; 2015 Sep 9Regional Isolation Drives Bacterial Diversification within Cystic Fibrosis Lungs.
26288390Sanders, Don B; Emerson, Julia; Ren, Clement L; Schechter, Michael S; Gibson, Ronald L; Morgan, Wayne; Rosenfeld, Margaret; EPIC Study GroupAnn Am Thorac Soc; 2015 AugEarly Childhood Risk Factors for Decreased FEV1 at Age Six to Seven Years in Young Children with Cystic Fibrosis.
26288277Damman, Christopher J; Brittnacher, Mitchell J; Westerhoff, Maria; Hayden, Hillary S; Radey, Matthew; Hager, Kyle R; Marquis, Sara R; Miller, Samuel I; Zisman, Timothy LPLoS One; 2015Low Level Engraftment and Improvement following a Single Colonoscopic Administration of Fecal Microbiota to Patients with Ulcerative Colitis.
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